Seuser Axel, Djambas Khayat Claudia, Negrier Claude, Sabbour Adly, Heijnen Lily
Private Practice for Prevention, Rehabilitation and Orthopaedics, Bonn, Germany.
Ho[Combining Circumflex Accent]tel Dieu de France Hospital, Beirut, Lebanon.
Blood Coagul Fibrinolysis. 2018 Sep;29(6):509-520. doi: 10.1097/MBC.0000000000000767.
: Early joint damage in patients with haemarthrosis often escapes diagnosis because of insufficient investigation of biomechanical changes. Arthropathy in haemophilia requires complex assessment with several tools. Considering the increased emphasis on an integrated approach to musculoskeletal (MSK) outcomes, re-evaluation of MSK assessment to address individual patient needs is warranted. To advise on the optimal use of current assessment tools and strategies for tailored MSK evaluation in patients with haemophilia. A panel of experts in haemophilic arthropathy evaluated internationally recognized assessment tools through published literature and personal expertise. Each tool was considered, scored and ranked for their utility in the clinical assessment of MSK damage. Subsequently, a patient evaluation table detailing advice on type and frequency of assessments for different patient populations was constructed. To obtain a complete MSK assessment, multiple tools must be used to ensure each criterion is evaluated. For patients with haemophilia, clinical examination of the joint, disease-specific structure/function scores, and activity/participation scores including quality of life are important, and should be performed on a regular basis according to age and clinical condition. Joint imaging is recommended in the prevention, diagnosis and follow-up of haemophilic arthropathy and should be used in conjunction with joint structure and function scores. An integrated approach to MSK assessment using combinations of tools will allow earlier management of dysfunction and may improve long-term outcomes. This approach could be used in long-term follow-up of all patients independent of age and disease stage, especially in children to prevent arthropathy.
血友病患者早期关节损伤常因对生物力学变化的调查不足而漏诊。血友病性关节病需要用多种工具进行综合评估。鉴于对肌肉骨骼(MSK)结局综合方法的日益重视,有必要重新评估MSK评估以满足个体患者需求。为血友病患者量身定制的MSK评估提供当前评估工具和策略的最佳使用建议。一组血友病性关节病专家通过已发表的文献和个人专业知识对国际认可的评估工具进行了评估。对每种工具在MSK损伤临床评估中的效用进行了考量、评分和排名。随后,构建了一个患者评估表,详细说明了针对不同患者群体的评估类型和频率建议。为了获得完整的MSK评估,必须使用多种工具以确保对每个标准进行评估。对于血友病患者,关节的临床检查、疾病特异性结构/功能评分以及包括生活质量在内的活动/参与评分很重要,应根据年龄和临床状况定期进行。建议在血友病性关节病的预防、诊断和随访中使用关节成像,并应与关节结构和功能评分结合使用。使用多种工具组合的MSK评估综合方法将有助于更早地处理功能障碍,并可能改善长期结局。这种方法可用于所有患者的长期随访,无论其年龄和疾病阶段如何,尤其是在儿童中预防关节病。