Jullian Lucas, Harrogate Suzanne Rachel, Harky Amer, Roberts Neil
Department of General Surgery, Homerton University Hospital, London, UK.
Department of Cardiac Surgery, Barts Heart Centre, St. Bartholomew's Hospital, London, UK.
BMJ Case Rep. 2018 Jul 19;2018:bcr-2018-224367. doi: 10.1136/bcr-2018-224367.
Papillary fibroelastomas are rare benign tumours arising from the cardiac endothelium. The rationale behind the treatment of fibroelastomas is to eliminate the risk of embolic events and the associated morbidity and mortality. These tumours present predominantly in males during the seventh decade of life and most commonly affect the aortic valve. We report a case of aortic valve papillary fibroelastoma with an atypical clinical presentation, treated with valve-sparing surgical excision. Our case highlights the management of this rare but serious condition and emphasises the need to develop clear guidelines regarding the treatment of asymptomatic patients with a papillary fibroelastoma.
乳头状纤维弹性瘤是一种罕见的起源于心脏内皮的良性肿瘤。治疗纤维弹性瘤的基本原理是消除栓塞事件风险以及相关的发病率和死亡率。这些肿瘤主要出现在70岁左右的男性中，最常累及主动脉瓣。我们报告一例具有非典型临床表现的主动脉瓣乳头状纤维弹性瘤病例，采用保留瓣膜的手术切除进行治疗。我们的病例突出了这种罕见但严重疾病的管理，并强调需要制定关于无症状乳头状纤维弹性瘤患者治疗的明确指南。
