伴有广泛毛囊性棘层松解、类似寻常型天疱疮的红皮病型毛发红糠疹：一例报告
Pityriasis Rubra Pilaris With Extensive Follicular Acantholysis Resembling Pemphigus Vulgaris: A Case Report.
作者信息
Lilo Mohammed T, Yan Shaofeng, Chapman Michael Shane, Linos Konstantinos
机构信息
Department of Pathology and Laboratory Medicine, Dartmouth-Hitchcock Medical Center and Geisel School of Medicine, Lebanon, NH.
Section of Dermatology, Department of Surgery, Dartmouth-Hitchcock Medical Center and Geisel School of Medicine, Lebanon, NH.
出版信息
Am J Dermatopathol. 2019 Jan;41(1):37-39. doi: 10.1097/DAD.0000000000001222.
Pityriasis rubra pilaris (PRP) is a rare, chronic, heterogeneous, papulosquamous inflammatory dermatosis of unknown etiology. Although erythematous scaly patches characterize the classic presentation of PRP, a broad range of clinical presentations has been reported. Histologically, PRP is characterized by psoriasiform acanthosis with alternating orthokeratosis and parakeratosis and rarely small acantholytic foci. In this article, we report a patient who presented with diffuse erythroderma and extensive acantholysis mimicking pemphigus vulgaris histologically.
红皮病型毛发红糠疹（PRP）是一种罕见的、慢性的、异质性的、病因不明的丘疹鳞屑性炎症性皮肤病。虽然红斑鳞屑斑块是PRP的典型表现，但也有广泛的临床表现报道。组织学上，PRP的特征是银屑病样棘层肥厚，伴有交替的正角化和角化不全，很少有小的棘层松解灶。在本文中，我们报告了一名患者，其表现为弥漫性红皮病，组织学上有广泛的棘层松解，酷似寻常型天疱疮。
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