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支气管内黏液瘤:一种罕见的病症。

Endobronchial Myxoma: An Uncommon Entity.

作者信息

Mukherjee Arindam, Agarwal Ritesh, Dhooria Sahajal, Singh Pawan, Bal Amanjit, Singh Harkant, Sehgal Inderpaul S

机构信息

Departments of Pulmonary Medicine.

Histopathology.

出版信息

J Bronchology Interv Pulmonol. 2018 Oct;25(4):335-339. doi: 10.1097/LBR.0000000000000503.

DOI:10.1097/LBR.0000000000000503
PMID:30048419
Abstract

A 31-year-old woman presented with progressive breathlessness since 1 year. Flexible bronchoscopy revealed a vascular tumor completely occluding the right main bronchus. A diagnosis of primary endobronchial myxoma was made. Tumor debulking was performed using rigid bronchoscopy. This enabled right lower lobectomy. A literature search yielded 12 cases of primary pulmonary myxoma, and only 2 previous reports of endobronchial myxoma. Most tumors were incidentally detected and were cured surgically. Endobronchial myxomas are rare and are usually asymptomatic. Treatment involves surgical excision. Rigid bronchoscopy serves as a bridge to surgery and can reduce the extent of surgery.

摘要

一名31岁女性自1年前起出现进行性呼吸困难。可弯曲支气管镜检查发现一个血管性肿瘤完全阻塞了右主支气管。诊断为原发性支气管内黏液瘤。使用硬支气管镜进行肿瘤减容。这使得能够进行右下肺叶切除术。文献检索发现12例原发性肺黏液瘤,仅有2例先前关于支气管内黏液瘤的报道。大多数肿瘤是偶然发现的,通过手术治愈。支气管内黏液瘤罕见,通常无症状。治疗包括手术切除。硬支气管镜可作为手术的桥梁,能减少手术范围。

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