T细胞大颗粒淋巴细胞白血病合并腹膜后脂肪肉瘤的治疗
Management of T-cell large granular lymphocyte leukemia and concurrent retroperitoneal liposarcoma.
作者信息
Bruce Nolan R, Tilley Zachary W, Carlson Jacob T, Barreto Andrade Juan Camilo
机构信息
Department of General Surgery, University of Arkansas for Medical Sciences, 4301 West Markham Street, Little Rock, AR, USA.
College of Medicine, University of Arkansas for Medical Sciences, 4301 West Markham Street, Little Rock, AR, USA.
出版信息
J Surg Case Rep. 2018 Jul 24;2018(7):rjy142. doi: 10.1093/jscr/rjy142. eCollection 2018 Jul.
T-cell large granular leukemia (T-LGL) is a rare lymphoproliferative disorder characterized by the clonal expansion of cytotoxic T lymphocytes. We present a unique case of T-LGL and concurrent retroperitoneal sarcoma occurring in a patient with long-standing rheumatoid arthritis. Pathology revealed a high-grade dedifferentiated liposarcoma. The diagnosis of T-LGL with a synchronous retroperitoneal sarcoma is a case that highlights the surgical management of these two rare conditions.
T细胞大颗粒淋巴细胞白血病（T-LGL）是一种罕见的淋巴增殖性疾病，其特征为细胞毒性T淋巴细胞的克隆性扩增。我们报告了一例独特的病例，一名患有长期类风湿性关节炎的患者同时发生了T-LGL和腹膜后肉瘤。病理检查显示为高级别去分化脂肪肉瘤。T-LGL合并同步腹膜后肉瘤的诊断是一个突出这两种罕见疾病外科治疗的病例。
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