脑实质内脉络丛乳头状瘤的快速恶性进展。
Rapid malignant progression of an intraparenchymal choroid plexus papillomas.
作者信息
Ruggeri Luca, Alberio Nicola, Alessandrello Raffaele, Cinquemani Giovanni, Gambadoro Cesare, Lipani Rita, Maugeri Rosario, Nobile Francesco, Iacopino Domenico Gerardo, Urrico Giovanni, Battaglia Roberto
机构信息
Unit of Neurosurgery, S. Elia Hospital, Caltanissetta, Italy.
Department of Experimental Biomedicine and Clinical Neurosciences, School of Medicine, Neurosurgical Clinic, University of Palermo, Italy.
出版信息
Surg Neurol Int. 2018 Jul 5;9:131. doi: 10.4103/sni.sni_434_17. eCollection 2018.
BACKGROUND
Choroid plexus tumors (CPTs) are rare neoplasms accounting for only 0.3-0.6% of all brain tumors in adults and 2-5% in children. The World Health Organization (WHO) classification describes three histological grades: grade I is choroid plexus papilloma (CPP), grade II is atypical papilloma, and grade III is the malignant form of carcinoma. In adults, CPTs rarely have a supratentorial localization.
CASE DESCRIPTION
Here we report a very rare case of an intraparenchymal parietal CPP with a rapid histological transition from grade I to grade III WHO in a 67-year-old man, in <7 months.
CONCLUSION
Because of the rarity of these oncotypes, descriptions of each new case are useful, mostly to consider this diagnostic entity in extraventricular brain tumors of adults, despite an unusual location.
背景
脉络丛肿瘤（CPTs）是罕见肿瘤，在成人所有脑肿瘤中仅占0.3 - 0.6%，在儿童中占2 - 5%。世界卫生组织（WHO）分类描述了三种组织学分级：I级为脉络丛乳头状瘤（CPP），II级为非典型乳头状瘤，III级为恶性癌形式。在成人中，CPTs很少发生幕上定位。
病例描述
在此我们报告一例非常罕见的病例，一名67岁男性，脑实质内顶叶CPP在不到7个月的时间里组织学上迅速从WHO I级转变为III级。
结论
由于这些肿瘤类型罕见，描述每一例新病例都很有用，主要是为了在成人脑室外肿瘤中考虑这一诊断实体，尽管其位置不寻常。
Zotero 插件