Hajji F, Moufid K, Ghoundale O, Touiti D
Department of Urology, Ibn Sina Military Hospital , Marrakech , Morocco.
Ann R Coll Surg Engl. 2018 Aug 16;100(8):e1-e3. doi: 10.1308/rcsann.2018.0141.
Crossed renal ectopia with fusion is an extremely rare congenital anomaly with few reported cases of pelviureteric junction obstruction, which often involves the crossed-over kidney. To our knowledge, we describe the second case in literature to report an uncrossed kidney with pelviureteric junction obstruction and giant hydronephrosis, which obstructs the pelviureteric junction of the crossed-over kidney. The grossly hydronephrotic kidney was found to be poorly functioning and an aberrant crossing vessel was considered to be potentially involved, raising both diagnostic and management challenges. By reporting this case, we aim to stress the importance of adequate mapping collecting systems, drainage patterns and vascular supply in such crossed fused anomalies.
交叉异位肾伴融合是一种极其罕见的先天性异常，肾盂输尿管连接处梗阻的报道病例很少，且常累及交叉异位肾。据我们所知，我们报道了文献中的第二例病例，该病例为未交叉的肾脏伴有肾盂输尿管连接处梗阻和巨大肾积水，后者梗阻了交叉异位肾的肾盂输尿管连接处。发现严重肾积水的肾脏功能不佳，且认为有一支异常交叉血管可能与之相关，这增加了诊断和治疗的挑战。通过报道此病例，我们旨在强调在这类交叉融合异常中充分描绘集合系统、引流模式和血管供应的重要性。
