Yang Deng-Ho, Yang Meng-Yin
Division of Rheumatology/Immunology/Allergy, Department of Internal Medicine, Taichung Armed-Forces General Hospital, Taichung 411, Taiwan.
Department of Laboratory, Taichung Armed Forces General Hospital, Taichung 411, Taiwan.
J Clin Med. 2018 Aug 22;7(9):230. doi: 10.3390/jcm7090230.
Evans syndrome is a rare disorder with presentations of autoimmune hemolytic anemia and immune thrombocytopenia, in the absence of any underlying cause. Here, we reported a case with a history of Evans syndrome for seven years. A persistent scrotal ulcer with severe pain occurred for two weeks. He called at our emergency room because of a painful, necrolytic cutaneous ulcer over the scrotal region. A biopsy showed sterile dermal neutrophilia with lymphocytic vasculitis, and pyoderma gangrenosum was impressed. The patient received steroid treatment and recovery after one month.
伊文氏综合征是一种罕见的疾病,表现为自身免疫性溶血性贫血和免疫性血小板减少症,且无任何潜在病因。在此,我们报告一例有七年伊文氏综合征病史的病例。患者阴囊出现持续两周的严重疼痛性溃疡。他因阴囊区域疼痛性、坏死性皮肤溃疡前来我们的急诊室就诊。活检显示无菌性真皮中性粒细胞增多伴淋巴细胞性血管炎,考虑为坏疽性脓皮病。患者接受了类固醇治疗,一个月后康复。