From the Baylor Scott & White Heart and Vascular Institute, the Departments of Pathology and Internal Medicine (Division of Cardiology), Baylor University Medical Center, Part of Baylor Scott & White Health, Dallas, Texas.
From the Baylor Scott & White Heart and Vascular Institute, the Departments of Pathology and Internal Medicine (Division of Cardiology), Baylor University Medical Center, Part of Baylor Scott & White Health, Dallas, Texas.
Am J Cardiol. 2018 Sep 15;122(6):1051-1061. doi: 10.1016/j.amjcard.2018.06.004. Epub 2018 Jun 22.
Although several electrocardiographic features of arrhythmogenic right ventricular cardiomyopathy (ARVC) (also called dysplasia) have been described, total 12-lead QRS voltage is not one of them. This report describes total 12-lead QRS voltage in 11 patients with ARVC who underwent orthotopic heart transplantation (OHT) because of progressively severe heart failure. Additionally, it illustrates the varied morphologic features of ARVC. The total 12-lead nonpaced QRS voltages before OHT ranged from 28 to 118 mm (mean 74 ± 32), and those in the paced tracings, from 33 to 129 mm (62 ± 32). The voltages are the lowest we have encountered among 12 previously reported cardiovascular conditions. The heart weights among the 11 ARVC patients ranged from 285 to 670 g (mean 448 ± 125). Very low 12-lead QRS voltage is characteristic of patients with ARVC with heart failure severe enough to warrant OHT, and thus may serve as a clue to its diagnosis.
尽管已经描述了致心律失常性右室心肌病（ARVC）（也称为发育不良）的几个心电图特征，但总 12 导联 QRS 电压并不是其中之一。本报告描述了 11 例因进行性严重心力衰竭而接受原位心脏移植（OHT）的 ARVC 患者的总 12 导联 QRS 电压。此外，还说明了 ARVC 的各种形态特征。OHT 前总 12 导联非起搏 QRS 电压范围为 28 至 118mm（平均 74±32），起搏描记中的电压范围为 33 至 129mm（62±32）。这些电压是我们在之前报告的 12 种心血管疾病中遇到的最低值。11 例 ARVC 患者的心脏重量范围为 285 至 670g（平均 448±125）。非常低的 12 导联 QRS 电压是心力衰竭严重到需要 OHT 的 ARVC 患者的特征，因此可能是其诊断的线索。
