Department of Metabolic Medicine, Graduate School of Medicine, Osaka University, Suita, Japan.
Ikuno Eye Center, Osaka City, Japan.
J Diabetes Investig. 2019 Mar;10(2):552-553. doi: 10.1111/jdi.12902. Epub 2018 Aug 27.
We present a case of a novel PAX6 heterozygous mutation with aniridia and insulin-dependent diabetes mellitus.To the best of our knowledge, this is the first case of its mutation with a complete loss of insulin secretory capacity. We believe that our letter will add new knowledge to diabetes mellitus associated with PAX6 mutations and might help us to understand the role of PAX6 in beta-cell development.
我们报告了一例新型 PAX6 杂合突变伴发无虹膜症和胰岛素依赖型糖尿病。据我们所知,这是首例该突变导致完全丧失胰岛素分泌能力的病例。我们相信,我们的病例报告将为 PAX6 突变相关糖尿病增添新的知识,并有助于我们理解 PAX6 在β细胞发育中的作用。