Pathan Iqbal Hussain, Bangash Sohail Khan, Zaki Saad Bader, Sheikh Abdul Sattar
Department of Cardiac Surgery, National Institute of Cardiovascular Diseases (NICVD), Karachi.
Department of Paeds Cardiology, National Institute of Cardiovascular Diseases (NICVD), Karachi.
J Coll Physicians Surg Pak. 2018 Sep;28(9):S154-S156. doi: 10.29271/jcpsp.2018.09.S154.
The arterial switch operation is considered as standard therapy for isolated D-transposition of the great arteries. However, in under-developed countries, patients still present with D-transposition of the great arteries beyond the neonatal age redering them unsuitable for anatomical repair. These children are often offered physiological repair, i.e. Senning or Mustard procedure. We describe our experience of a successful Senning procredure in a 4.6-year girl, who had atrial and visceral situs inversus totalis, dextrocardia and d-transposition of the great arteries. To our knowledge, this is the first reported case of this operation in a patient with such unique anatomy.
动脉调转术被认为是孤立性大动脉D型转位的标准治疗方法。然而,在不发达国家,仍有大动脉D型转位的患者超过新生儿期,这使得他们不适合进行解剖修复。这些儿童通常接受生理性修复,即森宁手术或马斯塔德手术。我们描述了我们在一名4.6岁女孩身上成功进行森宁手术的经验,该女孩患有心房和内脏全反位、右位心和大动脉D型转位。据我们所知,这是首例报道的对具有这种独特解剖结构的患者进行该手术的病例。