Van Thiel D H, Gartner L M, Thorp F K, Newman S L, Lindahl J A, Stoner E, New M I, Starzl T E
J Hepatol. 1986;3(1):42-8. doi: 10.1016/s0168-8278(86)80144-1.
The clinical history before transplantation and subsequent clinical and biochemical course of 3 children and one adult with hereditary tyrosinemia treated by orthotopic hepatic transplantation is described. All four patients are now free of their previous dietary restrictions and appear to be cured of both their metabolic disease and their hepatic neoplasm.
本文描述了3名儿童和1名成人遗传性酪氨酸血症患者原位肝移植术前的临床病史以及术后的临床和生化病程。所有4名患者现已摆脱先前的饮食限制，代谢疾病和肝肿瘤似乎均已治愈。
