Ting Jeannette W C, Kaur Sarbjit, Ogboli Malobi, Irani Kiri, Jester Andrea
Hands and Upper Limb Service, Birmingham Women's and Children's Hospital, Birmingham, UK.
Pediatr Dermatol. 2018 Nov;35(6):864-865. doi: 10.1111/pde.13674. Epub 2018 Sep 6.
Kindler disease is a type of epidermolysis bullosa associated with acral blistering, diffuse cutaneous atrophy, poikiloderma, mucosal stenosis, and photosensitivity. This is the first case report in the literature to describe constriction bands associated with Kindler disease causing ischemia of the fingertips requiring urgent release and full-thickness skin grafts. Dermatologists reviewing such patients need to be aware of this condition and refer to a children's hand surgeon early to avoid leaving patients with prolonged periods of pain.
金德勒病是一种大疱性表皮松解症，伴有肢端水疱、弥漫性皮肤萎缩、皮肤异色症、黏膜狭窄和光敏性。这是文献中首例描述与金德勒病相关的紧缩带导致指尖缺血，需要紧急松解和全厚皮片移植的病例报告。诊治此类患者的皮肤科医生需要了解这种情况，并尽早转诊给儿童手外科医生，以免患者长期遭受疼痛。
