Dave Tarjani Vivek, Cicinelli Maria Vittoria, Dave Vivek Pravin, Pappuru Rajeev Reddy, Naik Milind N, Mishra Dilip K
Socket, Anophthalmia and Orbitofacial Prosthesis Service, LV Prasad Eye Institute, Hyderabad, India.
Ophthalmic Plastic Surgery Service, LV Prasad Eye Institute, Hyderabad, India.
Ophthalmic Plast Reconstr Surg. 2018 Sep/Oct;34(5):e170-e172. doi: 10.1097/IOP.0000000000001200.
Congenital microphthalmos belongs to a spectrum of diseases ranging from true anophthalmos to congenital clinical anophthalmos to microphthalmos. These conditions are frequently associated with an orbitopalpebral cyst, and pathologically, this represents a failure in the closure of the embryonic fissure at the 7-14 mm stage of gestation. The cyst develops as an outpouching from the eyeball and is generally helpful as it provides a stimulus for the orbit to expand. The general management guideline is to retain the cyst till it provides a stimulus for the orbit to expand and then to consider aspiration and sclerotherapy once orbital expansion is achieved. However, in eyes that have visual potential, sclerotherapy is contraindicated. The authors present an unusual case of a mildly microphthalmic eye with visual potential and a communicating cyst that was excised with a good result. The challenges faced in the excision of the communicating cyst with a wide pedicle and the management of the case are highlighted.
先天性小眼症属于一系列疾病，范围从真性无眼球到先天性临床无眼球再到小眼症。这些情况常与眶睑囊肿相关，从病理角度来看，这代表着在妊娠7至14毫米阶段胚胎裂隙闭合失败。囊肿是从眼球向外突出形成的，通常是有益的，因为它能刺激眼眶扩张。一般的治疗原则是保留囊肿，直到它能刺激眼眶扩张，然后在眼眶扩张完成后考虑抽吸和硬化治疗。然而，对于有视觉潜力的眼睛，硬化治疗是禁忌的。作者介绍了一例不寻常的病例，患眼为轻度小眼症且有视觉潜力，伴有一个交通性囊肿，囊肿被切除且效果良好。文中强调了切除宽蒂交通性囊肿时面临的挑战以及该病例的处理情况。
