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韧带样纤维瘤病的最新进展

Current Update on Desmoid Fibromatosis.

作者信息

Ganeshan Dhakshinamoorthy, Amini Behrang, Nikolaidis Paul, Assing Matthew, Vikram Raghunandan

机构信息

From the Division of Diagnostic Imaging, Body Imaging Section.

Division of Diagnostic Imaging, The University of Texas MD Anderson Cancer Center, Houston, TX.

出版信息

J Comput Assist Tomogr. 2019 Jan-Feb;43(1):29-38. doi: 10.1097/RCT.0000000000000790.

DOI:10.1097/RCT.0000000000000790
PMID:30211798
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6331223/
Abstract

OBJECTIVE

The purpose of this article is to review the etiopathogenesis, molecular cytogenetics, histopathology, clinical features, and multimodality imaging features of desmoid fibromatosis. Recent advances in the management of desmoid fibromatosis will also be discussed.

CONCLUSIONS

Desmoid fibromatosis is a rare soft tissue neoplasm with a high incidence of local recurrence. Imaging plays an important role in the diagnosis and management of this disease.

摘要

目的

本文旨在综述韧带样纤维瘤病的病因发病机制、分子细胞遗传学、组织病理学、临床特征及多模态影像学特征。还将讨论韧带样纤维瘤病治疗的最新进展。

结论

韧带样纤维瘤病是一种罕见的软组织肿瘤，局部复发率高。影像学在该疾病的诊断和治疗中起着重要作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/74eb9eff0cff/nihms-1500783-f0025.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/75359b2b2bd2/nihms-1500783-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/a6660943b21a/nihms-1500783-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/49c9ff1ee812/nihms-1500783-f0004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/8089eafcd975/nihms-1500783-f0007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/f9dfd769df26/nihms-1500783-f0010.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/50230491193c/nihms-1500783-f0012.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/aed044bb9d3b/nihms-1500783-f0014.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/52fadcaad806/nihms-1500783-f0020.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/afde0fc5d16a/nihms-1500783-f0021.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/74eb9eff0cff/nihms-1500783-f0025.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/75359b2b2bd2/nihms-1500783-f0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/a6660943b21a/nihms-1500783-f0003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/49c9ff1ee812/nihms-1500783-f0004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/8089eafcd975/nihms-1500783-f0007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/f9dfd769df26/nihms-1500783-f0010.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/50230491193c/nihms-1500783-f0012.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/aed044bb9d3b/nihms-1500783-f0014.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/52fadcaad806/nihms-1500783-f0020.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/afde0fc5d16a/nihms-1500783-f0021.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f5ba/6331223/74eb9eff0cff/nihms-1500783-f0025.jpg

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