Bell Douglas Jw, He Cheng, Pauli John L, Naidoo Rishendran
1 Department of Cardiothoracic Surgery, The Prince Charles Hospital, Chermside, Australia.
2 Department of Anatomical Pathology, The Prince Charles Hospital, Chermside, Australia.
Asian Cardiovasc Thorac Ann. 2018 Sep;26(7):560-562. doi: 10.1177/0218492316675533. Epub 2016 Oct 18.
Maroteaux-Lamy syndrome is a very rare multisystem disorder. Cardiac valve surgery is common in these patients who present a unique set of perioperative and intraoperative challenges to the surgeon and treating team. We describe successful mitral valve replacement using an inverted aortic prosthesis in a 29-year-old lady with Maroteaux-Lamy syndrome, with a good result at 10 months.
马罗-拉米综合征是一种非常罕见的多系统疾病。心脏瓣膜手术在这些患者中很常见，他们给外科医生和治疗团队带来了一系列独特的围手术期和术中挑战。我们描述了一位29岁患有马罗-拉米综合征的女性患者使用倒置主动脉假体成功进行二尖瓣置换术，术后10个月效果良好。
