Ueki H, Inagaki Y, Kohda M, Takei Y
Hautarzt. 1986 Dec;37(12):673-5.
In a 14-year-old female patient with arteriovenous shunts (Stewart-Bluefarb syndrome), fist-sized cutaneous swelling, venous dilatation, blue-brown pigmentation and painful subcutaneous fingertip-sized nodules were noted on the right lower thigh. In addition to an arteriovenous malformation, bone hypertrophy, bone atrophy and after bone defects were observed in the involved area on X-ray examination. Histological examination revealed increased vascularity and vascular cavernous structures with endothelial swelling and extravasation of erythrocytes, but no malignant changes.
在一名患有动静脉分流(斯图尔特-布卢法布综合征)的14岁女性患者中,在右大腿下部发现了拳头大小的皮肤肿胀、静脉扩张、蓝褐色色素沉着以及疼痛的皮下指尖大小的结节。除动静脉畸形外,X线检查发现受累区域有骨肥大、骨萎缩及骨质缺损。组织学检查显示血管增多和血管海绵状结构,伴有内皮肿胀和红细胞外渗,但无恶性改变。