Yang L, Yang C Q
Division of Gastroenterology and Hepatology, Institute of Digestive Disease, Tongji Hospital, Tongji University School of Medicine, Shanghai 200065, China.
Zhonghua Gan Zang Bing Za Zhi. 2018 Jun 20;26(6):407-410. doi: 10.3760/cma.j.issn.1007-3418.2018.06.003.
Immunoglobulin G4-related disease (IgG4-RD) is an immune-mediated disease that share common pathologic, serologic and clinical features. IgG4- RD may include inflammatory pseudotumor, IgG4-related autoimmune hepatitis, and type 1 autoimmune pancreatitis mainly involving liver and clinically classified into three types. IgG4-related sclerosing cholangitis is a rare disease. It is frequently present in association with type 1 autoimmune pancreatitis, so it needs to be distinguishing from primary sclerosing cholangitis.
免疫球蛋白G4相关性疾病（IgG4-RD）是一种具有共同病理、血清学和临床特征的免疫介导性疾病。IgG4-RD可能包括炎性假瘤、IgG4相关性自身免疫性肝炎以及主要累及肝脏且临床分为三型的1型自身免疫性胰腺炎。IgG4相关性硬化性胆管炎是一种罕见疾病。它常与1型自身免疫性胰腺炎相关，因此需要与原发性硬化性胆管炎相鉴别。
