Zhang Jingqiao, Guo Xiaozhong, Li Hongyu, Shao Xiaodong, Deng Jiao, Liang Zhendong, Zhang Xia, Feng Ji, Lin Hao, Qi Xingshun
Department of Gastroenterology, General Hospital of Shenyang Military Area, Shenyang, China.
Department of Pharmacology, General Hospital of Shenyang Military Area, Shenyang, China.
Clin Exp Hepatol. 2018 Sep;4(3):205-209. doi: 10.5114/ceh.2018.78126. Epub 2018 Sep 10.
IgG4-related sclerosing cholangitis is a rare autoimmune liver disease. Biliary tract imaging, serum IgG4 concentration, and histopathological examination are the major diagnostic criteria for IgG4-related sclerosing cholangitis. In this paper, we report a male patient with yellowish skin, in whom classical liver-protection drugs were initially given, but the efficacy was poor. After that, IgG4-related sclerosing cholangitis was diagnosed, and he achieved a good response to steroid therapy.
IgG4相关性硬化性胆管炎是一种罕见的自身免疫性肝病。胆道成像、血清IgG4浓度及组织病理学检查是IgG4相关性硬化性胆管炎的主要诊断标准。在本文中，我们报告了一名皮肤发黄的男性患者，最初给予了经典的保肝药物，但疗效不佳。此后，该患者被诊断为IgG4相关性硬化性胆管炎，其对类固醇治疗反应良好。
