Ondari Joshua, Kinyanjui James, Miano Paul, Sang Edward, Oburu Ezekiel, Maru Michael
Orthopaedic Surgeon, Nakuru County Hospital, Nakuru, Kenya.
Orthopaedic Surgeon, St Marys Hospital, Nakuru, Kenya.
Pan Afr Med J. 2018 Jun 5;30:99. doi: 10.11604/pamj.2018.30.99.11969. eCollection 2018.
Femoral bifurcation and tibial hemimelia are rare anomalies described as a variant of Gollop-Wolfgang complex. This article presents a case of Gollop-Wolfgang complex without hand ectrodactyly. A 5-year old patient presented with bilateral tibial hemimelia and left femoral bifurcation. The patient's left limb lacked knee extensor mechanism, disarticulation was done. The right leg which had Jones type 2 tibia hemimelia was treated with tibiofibular synostosis. Currently patient is ambulant with prosthesis on the left limb and ankle foot orthosis on the right. In the absence of proximal tibial anlage, especially in patients with femoral bifurcation, the knee should be disarticulated. Tibiofibular synostosis is a good choice in the presence of a proximal tibial anlage with good quadriceps function.
股动脉分叉和胫骨半侧发育不全是罕见的畸形，被描述为戈洛普 - 沃尔夫冈复合体的一种变体。本文介绍了一例无手部缺指畸形的戈洛普 - 沃尔夫冈复合体病例。一名5岁患者表现为双侧胫骨半侧发育不全和左侧股动脉分叉。患者左下肢缺乏膝关节伸肌机制，进行了关节离断术。右侧为琼斯2型胫骨半侧发育不全，采用胫腓骨融合术治疗。目前，患者左下肢佩戴假肢、右下肢佩戴踝足矫形器可独立行走。在没有近端胫骨原基的情况下，尤其是存在股动脉分叉的患者，应进行膝关节离断术。在存在近端胫骨原基且股四头肌功能良好的情况下，胫腓骨融合术是一个不错的选择。
