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过敏性紫癜性脑血管炎:一例报告

Cerebral Vasculitis in Henoch-Schönlein Purpura: A Case Report.

作者信息

Akçaboy Meltem, Fidan Kibriya, Kandur Yaşar, Isiyel Emel, Büyükkaragöz Bahar, Bakkaloğlu Ezgü Sevcan Azime, Buyan Necla, Hasanoğlu Enver, Söylemezoğlu Oğuz

机构信息

Department of Pediatric Nephrology, Medical Faculty of Gazi University, Ankara, Turkey.

出版信息

Arch Rheumatol. 2017 Mar 24;32(3):264-267. doi: 10.5606/ArchRheumatol.2017.6225. eCollection 2017 Sep.

DOI:10.5606/ArchRheumatol.2017.6225
PMID:30375537
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6190959/
Abstract

Henoch-Schönlein purpura is a common form of systemic small vessel vasculitis in childhood. Although headache and behavioral changes have been described in a significant proportion of children with Henoch-Schönlein purpura, severe neurological complications are rare. In this article, we report a case of central vasculitis in a four-year-old boy who presented with hemiplegia and aphasia. The treatment options for cerebral vasculitis of Henoch-Schönlein purpura are numerous but controversial in pediatric patients. Our patient was successfully treated by pulse methylprednisolone and pulse cyclophosphamide. The patient was followed-up for four years without any sequel.

摘要

过敏性紫癜是儿童期常见的系统性小血管炎形式。虽然相当一部分过敏性紫癜患儿有头痛和行为改变的描述,但严重的神经系统并发症很少见。在本文中,我们报告了一例4岁男孩的中枢性血管炎病例,该患儿表现为偏瘫和失语。过敏性紫癜性脑血管炎的治疗选择众多,但在儿科患者中存在争议。我们的患者通过静脉注射甲泼尼龙和静脉注射环磷酰胺成功治愈。该患者随访4年无任何后遗症。

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本文引用的文献

1
Could serum pentraxin 3 levels and IgM deposition in skin biopsies predict subsequent renal involvement in children with Henoch-Schönlein purpura?血清五聚素3水平和皮肤活检中的IgM沉积能否预测过敏性紫癜患儿随后的肾脏受累情况?
Pediatr Nephrol. 2015 Jun;30(6):969-74. doi: 10.1007/s00467-014-3026-x. Epub 2014 Dec 28.
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Pediatric vasculitis.儿科血管炎。
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3
Henoch-Schönlein purpura in childhood: treatment and prognosis. Analysis of 425 cases over a 5-year period.儿童过敏性紫癜:治疗和预后。5 年期间 425 例病例分析。
Clin Rheumatol. 2010 Apr;29(4):369-74. doi: 10.1007/s10067-009-1329-2. Epub 2009 Dec 23.
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Clinical practice: Diagnosis and management of Henoch-Schönlein purpura.临床实践:过敏性紫癜的诊断与管理。
Eur J Pediatr. 2010 Jun;169(6):643-50. doi: 10.1007/s00431-009-1101-2. Epub 2009 Dec 12.
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Nervous system dysfunction in Henoch-Schonlein syndrome: systematic review of the literature.过敏性紫癜性肾炎患者神经系统损害:文献系统综述
Rheumatology (Oxford). 2009 Dec;48(12):1524-9. doi: 10.1093/rheumatology/kep282. Epub 2009 Sep 21.
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Cerebral vasculitis and intracerebral hemorrhage in Henoch-Schönlein purpura treated with plasmapheresis.采用血浆置换治疗的过敏性紫癜性脑血管炎和脑出血
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Cerebral vasculitis in Henoch-Schönlein purpura: MRI and MRA findings, treated with plasmapheresis alone.过敏性紫癜性脑血管炎:MRI和MRA表现,单纯血浆置换治疗
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Neurologic manifestations of Schoenlein-Henoch purpura: report of three cases and review of the literature.过敏性紫癜的神经系统表现:三例报告及文献复习
Pediatrics. 1985 Apr;75(4):687-92.
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Neurologic manifestations of Schönlein-Henoch purpura.过敏性紫癜的神经系统表现。
Acta Paediatr Scand. 1991 Mar;80(3):339-42. doi: 10.1111/j.1651-2227.1991.tb11859.x.