Kouadria R, Si Ali A, Aidouni Y, Maaz W, Mhamdi C
Department of neurosurgery and radiology, faculty of Medicine, UDL Sidi Bel Abbes, Algeria.
Department of neurosurgery and radiology, faculty of Medicine, UDL Sidi Bel Abbes, Algeria.
Neurochirurgie. 2018 Dec;64(6):442-444. doi: 10.1016/j.neuchi.2018.08.005. Epub 2018 Nov 2.
Intramedullary spinal cord lipomas (IMSCL) are a rare entity, accounting for less than 1% of spinal tumors. Most cases are associated with lumbosacral dysraphism and occur predominantly in the pediatric population.
We report the case of an isolated bipolar lipoma, which was very large in the cervicodorsal region and small in the conus medularis. The patient was a 9-years-old male who had muscle weakness for approximately 6 months. MRI showed a hyperintense lesion on T1, which was less intense on T2, without contrast enhancement at the cervicodorsal location and the conus medularis. At his admission, the patient experienced severe decompensation with flaccid tetraplegia and abdominal respiration. He immediately underwent decompression and partial resection of the cervical lesion. The anatomical pathology evaluation confirmed the diagnosis of a lipoma.
DISCUSSION/CONCLUSION: The possibility of quality resection of intramedullary spinal cord lipomas is controversial due to the lack of a cleavage plane with the anterior tracts. Any attempt at total resection would expose the patient to the risk of neurological worsening which is often irreversible. In our case, the surgical indication was self-imposed, the main objective of which was decompression.
脊髓髓内脂肪瘤(IMSCL)是一种罕见的疾病,占脊柱肿瘤的比例不到1%。大多数病例与腰骶部脊柱裂相关,主要发生在儿童人群中。
我们报告一例孤立性双极脂肪瘤病例,该脂肪瘤在颈胸段区域很大,而在脊髓圆锥处较小。患者为一名9岁男性,有大约6个月的肌肉无力症状。磁共振成像(MRI)显示在T1加权像上有一个高信号病变,在T2加权像上信号强度较低,在颈胸段位置和脊髓圆锥处无强化。入院时,患者出现严重失代偿,伴有弛缓性四肢瘫和腹式呼吸。他立即接受了颈椎病变的减压和部分切除术。解剖病理学评估证实为脂肪瘤。
讨论/结论:由于与前束缺乏分离平面,脊髓髓内脂肪瘤能否进行高质量切除存在争议。任何全切尝试都会使患者面临神经功能恶化的风险,而这种恶化往往是不可逆的。在我们的病例中,手术指征是自行确定的,其主要目的是减压。