Lim Mi Hee, Sung Si Chan, Kim Hyung Tae, Choi Kwang Ho, Lee Hyoung Doo, Kim Geena
Department of Thoracic and Cardiovascular Surgery, Pusan National University Yangsan Hospital, Research Institute for Convergence of Biomedical Science and Technology, Pusan National University Yangsan Hospital.
Department of Pediatric Cardiology, Pusan National University Yangsan Hospital, Research Institute for Convergence of Biomedical Science and Technology, Pusan National University Yangsan Hospital.
Korean J Thorac Cardiovasc Surg. 2018 Oct;51(5):356-359. doi: 10.5090/kjtcs.2018.51.5.356. Epub 2018 Oct 5.
We report a case of successful repair of truncus arteriosus (TA) associated with complete atrioventricular septal defect (c-AVSD) using a staged approach. TA associated with c-AVSD is a very rare congenital cardiac anomaly. No report of successful staged repair in South Korea has yet been published. We performed bilateral pulmonary artery banding when the patient was 33 days old, and total correction using an extracardiac conduit was performed at the age of 18 months. The patient recovered uneventfully and is doing well.
我们报告了一例采用分期手术成功修复与完全性房室间隔缺损（c-AVSD）相关的动脉干（TA）的病例。与c-AVSD相关的TA是一种非常罕见的先天性心脏异常。韩国尚未有成功分期修复的报道。患者33日龄时进行了双侧肺动脉环扎术，18个月大时使用心外管道进行了完全矫正。患者恢复顺利，情况良好。
