Godil Ansab, Ali Mallick Muhammad Saad, Khetpal Akash, Godil Faizan Jabir, Adam Arsalan Majeed, Mallick Muhammad Jawaid
Dow University of Health Sciences.
Oncology Department, Bait-ul-Sukoon Cancer Hospital, Karachi, Pakistan.
J Pak Med Assoc. 2018 Nov;68(11):1708-1710.
Primary mediastinal synovial sarcomas are very rare occurrences with only a few cases reported in literature to date. We present a similar case in an 18-year old male which proved challenging to diagnose and treat. Radiological imaging and tru-cut biopsy results gave rise to suspicion of an unusual malignancy. The sarcoma under went en bloc resection and subsequent immunohistochemical staining confirmed the diagnosis of synovial sarcoma. The patient was put on adjuvant chemotherapy after surgery to prevent recurrence. The purpose of this case report is to assist oncologists in the diagnosis and clinical management of this rare tumour.
原发性纵隔滑膜肉瘤非常罕见,迄今为止文献中仅报道了少数病例。我们报告了一名18岁男性的类似病例,该病例在诊断和治疗上颇具挑战性。放射影像学和粗针活检结果引发了对一种不寻常恶性肿瘤的怀疑。该肉瘤进行了整块切除,随后的免疫组织化学染色证实了滑膜肉瘤的诊断。患者术后接受辅助化疗以预防复发。本病例报告的目的是帮助肿瘤学家对这种罕见肿瘤进行诊断和临床管理。