Saavedra Melina J, Mozzi Javier, Nápoli Natalia, Villa Alejandra, Barretta Jorge, Marantz Pablo
Departamento de Pediatría, Servicio de Cardiología Pediátrica, Hospital Italiano de Buenos Aires.
Servicio de Cirugía Cardiovascular Pediátrica, Hospital Italiano de Buenos Aires.
Arch Argent Pediatr. 2018 Dec 1;116(6):e789-e792. doi: 10.5546/aap.2018.eng.e789.
The anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is a rare entity that has an incidence of 0.002 % and can potentially cause sudden death. Unlike to the anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA), usually presented with myocardial ischemia and heart failure; the diagnosis of ARCAPA is often incidental during evaluation of a heart murmur. We report a case of a 6 months old female patient referred to us with a cardiac murmur and a suspicion of coronary fistula. For a proper diagnostic assessment an echocardiogram, a computed tomography angiography and a cardiac catheterization were requested. A small ostium secundum-type atrial septal defect (ASD) and an ARCAPA were revealed. At 11 months old, the patient was scheduled for corrective cardiovascular surgery. The aim of this report is to describe a low incidence and potentially fatal disease.
右冠状动脉起源于肺动脉（ARCAPA）是一种罕见的疾病，发病率为0.002%，可能导致猝死。与通常表现为心肌缺血和心力衰竭的左冠状动脉起源于肺动脉（ALCAPA）不同；ARCAPA的诊断通常是在评估心脏杂音时偶然发现的。我们报告一例6个月大的女性患者，因心脏杂音和疑似冠状动脉瘘转诊至我院。为了进行正确的诊断评估，我们要求进行超声心动图、计算机断层血管造影和心导管检查。结果发现一个小型继发孔型房间隔缺损（ASD）和ARCAPA。患者11个月大时，计划进行心血管矫正手术。本报告的目的是描述一种发病率低且可能致命的疾病。
