Patwardhan Pranav Pramod, Goel Naina Atul
Department of Pathology, Seth G. S. Medical College and K. E. M. Hospital, Mumbai, Maharashtra, India.
Asian J Neurosurg. 2018 Oct-Dec;13(4):1285-1287. doi: 10.4103/ajns.AJNS_134_18.
Rosai-Dorfman disease (RDD) is a benign histioproliferative disorder characterized by generalized lymphadenopathy, weakness, anemia, and rarely extranodal involvement. The disease affects the central nervous system (CNS) very rarely and at a relatively older age. Isolated intracranial involvement is very rare. RDD tends to present as dural masses mimicking meningioma, though very rare case reports describe isolated parenchymal involvement in the CNS. Only one case of intraventricular RDD has been described so far to the best of our knowledge. We present a very rare presentation of this disease as an isolated intraventricular presentation in the region of the atria of the lateral ventricles.
罗萨伊-多夫曼病（RDD）是一种良性组织细胞增生性疾病，其特征为全身性淋巴结病、虚弱、贫血，极少有结外受累情况。该疾病极少累及中枢神经系统（CNS），且发病年龄相对较大。孤立性颅内受累非常罕见。RDD往往表现为模仿脑膜瘤的硬脑膜肿块，不过仅有极少数病例报告描述了CNS内的孤立性实质受累情况。据我们所知到目前为止仅描述过1例脑室型RDD。我们报告了该疾病一种非常罕见表现，即侧脑室心房区域出现孤立性脑室型表现。
