Akbayrak Hakan, Tekumit Hayrettin
Department of Cardiovascular Surgery, Faculty of Medicine, Selcuk University, Konya, Turkey. Email:
Department of Cardiovascular Surgery, Faculty of Medicine, Bezmialem University, Istanbul, Turkey.
Cardiovasc J Afr. 2019;30(1):e4-e6. doi: 10.5830/CVJA-2018-052. Epub 2018 Nov 20.
Chronic thromboembolic pulmonary hypertension (CTEPH) is a potentially correctable cause of secondary pulmonary hypertension. Surgical treatment remains the primary treatment for patients with CTEPH. Pulmonary thromboendarterectomy (PEA) with deep hypothermic circulatory arrest is the standard and recommended surgical technique for the treatment of these patients. The prevalence of CTEPH after an acute pulmonary thromboembolism (PTE) has been found in various studies to be between 0.6 and 8.8%. Mortality rates in elective PEA cases with CTEPH are reported to be between 1.9 and 4.5%. We report on a 50-year-old female patient with combined inherited thrombophilia, including protein C and protein S deficiencies, who was diagnosed with CTEPH and was successfully treated with pulmonary thromboendarterectomy.
慢性血栓栓塞性肺动脉高压（CTEPH）是继发性肺动脉高压的一个潜在可纠正病因。手术治疗仍是CTEPH患者的主要治疗方法。采用深低温循环停止的肺动脉血栓内膜剥脱术（PEA）是治疗这些患者的标准且推荐的手术技术。在各项研究中发现，急性肺血栓栓塞症（PTE）后CTEPH的患病率在0.6%至8.8%之间。据报道，CTEPH择期PEA病例的死亡率在1.9%至4.5%之间。我们报告了一名50岁的女性患者，她患有包括蛋白C和蛋白S缺乏在内的遗传性易栓症合并症，被诊断为CTEPH，并通过肺动脉血栓内膜剥脱术成功治愈。
