Karthigeyan Madhivanan, Malik Puneet, Garg Sumit, Radotra Bishan D, Salunke Pravin, Sunil Narasimhaiah, Kumar Narendra
Department of Neurosurgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
Department of Neurosurgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
World Neurosurg. 2019 Feb;122:500-504. doi: 10.1016/j.wneu.2018.11.082. Epub 2018 Nov 19.
Low-grade fibromyxoid sarcoma (LGFMS), an uncommon soft tissue tumor, generally occurs in extremities and is characterized by an aggressive clinical course with frequent recurrences. Primary intracranial occurrence of LGFMS is rare. The few existing descriptions present the clinicopathologic aspects of LGFMS and lack information from a radiologic perspective. In these reports, the lesions appeared solid on imaging.
In a 45-year-old woman, a falx-based lesion with solid-cystic radiologic appearance that turned out to be LGFMS on histopathology. The patient's clinical follow-up (2 years) is presented along with a literature review of other primary central nervous system cases.
This report emphasizes the radiologic aspects of LGFMS and describes an atypical solid-cystic appearance of this uncommon central nervous system tumor. This adds another facet to the imaging of LGFMS. Although rare, LGFMS can form a differential diagnosis of dural-based lesions.
低度纤维黏液样肉瘤（LGFMS）是一种罕见的软组织肿瘤，通常发生于四肢，临床病程呈侵袭性，复发频繁。原发性颅内LGFMS罕见。现有的少数描述呈现了LGFMS的临床病理特征，但缺乏放射学方面的信息。在这些报告中，病变在影像学上表现为实性。
一名45岁女性，镰旁病变在放射学上表现为实性-囊性，组织病理学结果显示为LGFMS。报告了该患者的2年临床随访情况，并对其他原发性中枢神经系统病例进行了文献综述。
本报告强调了LGFMS的放射学特征，并描述了这种罕见的中枢神经系统肿瘤非典型的实性-囊性表现。这为LGFMS的影像学表现增添了新的内容。尽管罕见，但LGFMS可作为硬膜病变的鉴别诊断之一。
