一例表现为感觉运动性多发性神经病的类固醇抵抗性桥本脑病病例。
A case of steroid-resistance Hashimoto's encephalopathy presenting with sensorimotor polyneuropathy.
作者信息
Emeksiz Serhat, Kutlu Nurettin Onur, Alaçakır Nuri, Çaksen Hüseyin
机构信息
Division of Pediatric Critical Care, Necmettin Erbakan University, Meram Faculty of Medicine, Konya, Turkey.
Division of Pediatric Neurology, Department of Pediatrics, Necmettin Erbakan University, Meram Faculty of Medicine, Konya, Turkey.
出版信息
Turk J Pediatr. 2018;60(3):310-314. doi: 10.24953/turkjped.2018.03.012.
Emeksiz S, Kutlu NO, Alaçakır N, Çaksen H. A case of steroid-resistance Hashimoto's encephalopathy presenting with sensorimotor polyneuropathy. Turk J Pediatr 2018; 60: 310-314. Hashimoto`s encephalopathy (HE) is a rare, auto-immune disease characterized by symptoms of acute or subacute encephalopathy associated with increased anti-thyroid antibody levels. The course of most HE cases is relapsing and remitting, which is similar to that of vasculitis and stroke. Steroids are the first line treatment in HE. In steroid non-responders other immunomodulatory therapies or plasmapheresis could be applied. We report a case of steroid-resistance HE with sensorimotor polyneuropathy, as a rare presentation of this disorder. Our case showed that HE may present with sensorimotor polyneuropathy; therefore HE should be considered in the differential diagnoses of polyneuropathy.
埃梅克西兹·S、库特卢·N·O、阿拉恰基尔·N、恰克森·H。一例表现为感觉运动性多神经病的类固醇抵抗性桥本脑病。《土耳其儿科学杂志》2018年；60: 310 - 314。桥本脑病（HE）是一种罕见的自身免疫性疾病，其特征为与抗甲状腺抗体水平升高相关的急性或亚急性脑病症状。大多数HE病例的病程呈复发缓解型，这与血管炎和中风相似。类固醇是HE的一线治疗药物。对于类固醇无反应者，可应用其他免疫调节疗法或血浆置换。我们报告一例伴有感觉运动性多神经病的类固醇抵抗性HE病例，作为该疾病的一种罕见表现形式。我们的病例表明，HE可能表现为感觉运动性多神经病；因此，在多神经病的鉴别诊断中应考虑HE。
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