Kiefer Michael, Bonarrigo Kelly, Quatman-Yates Catherine, Fowler Amanda, Horn Paul S, Wong Brenda L
Department of Pediatrics (Drs Kiefer and Wong), University of Massachusetts Medical School, Worcester, Massachusetts; Division of Occupational Therapy and Physical Therapy (Drs Kiefer, Bonarrigo, Quatman-Yates, and Fowler) and Division of Neurology (Drs Kiefer, Bonarrigo, Fowler, Horn, and Wong), Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio; Department of Pediatrics (Dr Horn), University of Cincinnati College of Medicine, Cincinnati, Ohio; Department of Physical Therapy (Dr Quatman-Yates), The Ohio State University, Columbus, Ohio.
Pediatr Phys Ther. 2019 Jan;31(1):61-66. doi: 10.1097/PEP.0000000000000553.
This study characterizes the progressive loss of ankle dorsiflexion range of motion in boys with Duchenne muscular dystrophy (DMD), the relationship to functional decline, and the implications for physical therapy management.
Longitudinal data for 332 boys with DMD were extracted from medical records and analyzed. Summary statistics for age, number of visits, ankle dorsiflexion measures, and North Star Ambulatory Assessment (NSAA) scores were computed.
Ankle dorsiflexion motion ranged from -32.5 to 25 degrees. Progression of ankle contractures is demonstrated by a trend line: slope -1.43 per year. NSAA score was estimated to decline approximately 0.23 points per 1 degree of ankle dorsiflexion lost.
The results of this study describe the progression of ankle contractures and functional decline in DMD. The findings may help inform decisions regarding interventions to support participants with DMD and their families.
本研究描述了杜氏肌营养不良症（DMD）男孩踝关节背屈活动范围的渐进性丧失、与功能下降的关系以及对物理治疗管理的影响。
从医疗记录中提取332名DMD男孩的纵向数据并进行分析。计算年龄、就诊次数、踝关节背屈测量值和北极星动态评估（NSAA）分数的汇总统计数据。
踝关节背屈活动范围为-32.5度至25度。踝关节挛缩的进展通过趋势线显示：每年斜率为-1.43。估计踝关节背屈每丧失1度，NSAA分数大约下降0.23分。
本研究结果描述了DMD患者踝关节挛缩和功能下降的进展情况。这些发现可能有助于为支持DMD患者及其家庭的干预措施决策提供参考。
