多形性横纹肌肉瘤转移至小肠导致肠套叠：一例报告
Pleomorphic rhabdomyosarcoma metastasis to small intestine causing intussusception: A case report.
作者信息
Xi Shiwen, Tong Weihua
机构信息
Department of Gastric and Colorectal Surgery, The First Affiliated Hospital of Jilin University, Changchun, Jilin, China.
出版信息
Medicine (Baltimore). 2018 Dec;97(51):e13648. doi: 10.1097/MD.0000000000013648.
RATIONALE
Pleomorphic rhabdomyosarcoma (PRMS) is a rare soft tissue malignancy which is frequently misdiagnosed and associated with metastasis to the lungs, lymph nodes, and bone marrow. Case studies are needed to improve the awareness of the disease and our understanding of it.
PATIENT CONCERNS
In this study, we present a case of a 36-year-old man with a lesion on the right back shoulder. Lesion was confirmed by magnetic resonance imaging (MRI) around the right armpit, subscapularis, deltoid, and infraspinatus muscle, with oozing surrounding soft tissues.
DIAGNOSIS
The tumor was diagnosed as PRMS which metastasized to the intestine, where it caused intussusception.
INTERVENTIONS
The patient was treated by complete surgery in combination with neo-adjuvant chemotherapy including ifosfamide and epirubicin.
OUTCOME
The patient remained alive 6 months after the treatment with no recurrence and metastasis.
LESSON
PRMS can be aggressive, and surgical treatment in combination with multidrug chemotherapy can be used in the management.
原理
多形性横纹肌肉瘤（PRMS）是一种罕见的软组织恶性肿瘤，常被误诊，且易转移至肺、淋巴结和骨髓。需要通过病例研究来提高对该疾病的认识以及我们对它的了解。
患者情况
在本研究中，我们报告一例36岁男性，其右后肩部有一病灶。磁共振成像（MRI）证实病灶位于右腋窝、肩胛下肌、三角肌和冈下肌周围，周围软组织有渗出。
诊断
该肿瘤被诊断为PRMS，已转移至肠道并导致肠套叠。
干预措施
患者接受了完整手术，并联合使用异环磷酰胺和表柔比星进行新辅助化疗。
结果
治疗6个月后患者存活，无复发和转移。
经验教训
PRMS可能具有侵袭性，手术治疗联合多药化疗可用于其治疗。
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