睾丸旁多形性横纹肌肉瘤：两例报告

Paratesticular pleomorphic rhabdomyosarcoma: a report of two cases.

作者信息

Boulma Rami, Gargouri Mohamed Mourad, Sallemi Ahmed, Chlif Mohamed, Fitouri Zouhaier, Kallel Yosri, Nouira Yassine

机构信息

Department of Urology, La Rabta University Hospital, 1007 Tunis, Tunisia.

出版信息

Case Rep Urol. 2013;2013:807979. doi: 10.1155/2013/807979. Epub 2013 Feb 12.

DOI:10.1155/2013/807979

PMID:23476881

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3583059/

Abstract

Pleomorphic rhabdomyosarcoma (RMS) is a rare tumor with an aggressive behavior, described mainly in adulthood. Herein we present two cases of paratesticular pleomorphic RMS in 71- and 16-year-old patients with metastases at initial diagnosis. Histological, immunohistochemical, and ultrastructural findings were essential to confirm diagnosis. Few months after radical orchiectomy, both patients died before or just after starting adjuvant chemotherapy.

摘要

多形性横纹肌肉瘤（RMS）是一种罕见的侵袭性肿瘤，主要见于成年人。在此我们报告两例睾丸旁多形性RMS病例，患者分别为71岁和16岁，初诊时已有转移。组织学、免疫组化及超微结构检查结果对确诊至关重要。根治性睾丸切除术后数月，两名患者均在开始辅助化疗前或化疗刚开始时死亡。