Saracino Dario, Allegorico Lia, Barbarulo Anna Maria, Pollo Bianca, Giaccone Giorgio, D'Amico Alessandra, D'Incerti Ludovico, Bugiani Orso, Di Iorio Giuseppe, Sampaolo Simone, Melone Mariarosa Anna Beatrice
a Second Division of Neurology , Center for Rare Neurological and Neuromuscular Diseases & Inter University Center for Research in Neurosciences, Department of Advanced Medical and Surgical Sciences, University of Campania Luigi Vanvitelli , Naples , Italy.
b Division of Neurology V - Neuropathology , Fondazione IRCCS Istituto Neurologico Carlo Besta , Milan , Italy.
Neurocase. 2018 Oct-Dec;24(5-6):238-241. doi: 10.1080/13554794.2018.1561898. Epub 2018 Dec 25.
Behçet's disease is a chronic inflammatory disorder manifesting as a vasculitis that affects arteries and veins of any size. Up to 44% of cases may also present with neurological symptoms, thus defining Neuro-Behçet's disease. We describe a case of Neuro-Behçet's disease characterized by progressive behavioral and cognitive deterioration prevailing over other neurological symptoms, without evident systemic involvement.
白塞病是一种慢性炎症性疾病,表现为血管炎,可累及任何大小的动静脉。高达44%的病例也可能出现神经症状,从而定义为神经白塞病。我们描述了一例以进行性行为和认知衰退为主,而非其他神经症状,且无明显全身受累的神经白塞病病例。