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[术中发现诊断先天性单叶主动脉瓣]

[Congenital Unicuspid Aortic Valve Diagnosed by Intraoperative Findings].

作者信息

Sasaki Yasuyuki, Sakaguchi Masanori, Bito Yasuyuki, Suehiro Yasuo, Nishiya Kenta, Inno Goki, Aratame Atsutaka

机构信息

Department of Cardiovascular Surgery, Osaka City General Hospital, Osaka, Japan.

出版信息

Kyobu Geka. 2018 Dec;71(13):1081-1083.

PMID:30587746
Abstract

A unicuspid aortic valve is an extremely rare congenital aortic valvular abnormality. We herein present 2 cases of unicuspid aortic valve diagnosed based on intraoperative findings. In case 1, a 75-year-old man was admitted to our hospital because of severe aortic regurgitation. We performed aortic valve replacement using a bioprosthetic valve, and a unicuspid aortic valve was definitively diagnosed according to the intraoperative findings. In case 2, a 54-year-old man developed dyspnea due to severe aortic stenosis. Aortic valve replacement using mechanical valve was performed, and we were able to diagnose unicuspid aortic valve intraoperatively. Achieving a preoperative definitive diagnosis of congenital unicuspid aortic valve by transthoracic echocardiography is reportedly difficult;however, transesophageal echocardiography may be effective for preoperative definitive diagnosis.

摘要

单叶主动脉瓣是一种极其罕见的先天性主动脉瓣异常。我们在此报告2例根据术中发现确诊的单叶主动脉瓣病例。病例1,一名75岁男性因严重主动脉瓣反流入院。我们使用生物瓣膜进行了主动脉瓣置换术,并根据术中发现明确诊断为单叶主动脉瓣。病例2,一名54岁男性因严重主动脉瓣狭窄出现呼吸困难。进行了机械瓣膜主动脉瓣置换术,术中我们得以诊断出单叶主动脉瓣。据报道,经胸超声心动图术前明确诊断先天性单叶主动脉瓣很困难;然而,经食管超声心动图可能对术前明确诊断有效。

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