Suppr超能文献

Loeys-Dietz 综合征 5 岁男童行保留瓣膜的主动脉根部和主动脉弓置换术。

Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome.

机构信息

Department of Pediatrics, Sahloul Teaching Hospital, University of Sousse, Sousse, Tunisia.

Department of Radiology, Sahloul Teaching Hospital, University of Sousse, Sousse, Tunisia.

出版信息

Eur J Cardiothorac Surg. 2019 Aug 1;56(2):409-411. doi: 10.1093/ejcts/ezy446.

Abstract

In this study, we describe the case of a 5-year-old boy who presumably presented with Loeys-Dietz syndrome. A huge aneurysm of the ascending aorta and the aortic arch extended beyond the left subclavian artery and was accompanied by a slight narrowing of the aortic isthmus.

摘要

在本研究中,我们描述了一例 5 岁男孩,推测其患有洛伊氏迪茨综合征。升主动脉和主动脉弓的巨大动脉瘤延伸至左锁骨下动脉以外,并伴有主动脉峡部的轻微狭窄。

相似文献

1
Valve-sparing aortic root and aortic arch replacement in a 5-year-old boy with Loeys-Dietz syndrome.
Eur J Cardiothorac Surg. 2019 Aug 1;56(2):409-411. doi: 10.1093/ejcts/ezy446.
2
Valve-sparing replacement of the ascending aorta and aortic arch in a child with Loeys-Dietz syndrome.
Eur J Cardiothorac Surg. 2012 May;41(5):1184-5. doi: 10.1093/ejcts/ezr235. Epub 2012 Jan 6.
3
Valve-sparing replacement of the aortic root for a 2-year-old child with Loeys-Dietz syndrome.
Cardiol Young. 2010 Feb;20(1):94-6. doi: 10.1017/S1047951109991557. Epub 2009 Oct 23.
4
Total arch replacement procedure in a child with Loeys-Dietz syndrome.
Eur J Cardiothorac Surg. 2012 May;41(5):1186. doi: 10.1093/ejcts/ezs003. Epub 2012 Feb 9.
5
Early clinical outcomes and molecular smooth muscle cell phenotyping using a prophylactic aortic arch replacement strategy in Loeys-Dietz syndrome.
J Thorac Cardiovasc Surg. 2023 Nov;166(5):e332-e376. doi: 10.1016/j.jtcvs.2023.07.023. Epub 2023 Jul 25.
6
Repair of an aneurysm of the ascending aorta and arch in an infant with Loeys-Dietz syndrome.
J Card Surg. 2018 May;33(5):286-288. doi: 10.1111/jocs.13605. Epub 2018 Apr 23.
7
Valve-sparing aortic root replacement in Loeys-Dietz syndrome.
Ann Thorac Surg. 2011 Aug;92(2):556-60; discussion 560-1. doi: 10.1016/j.athoracsur.2011.04.003.
8
Thoracoabdominal aortic replacement in a 6-year-old boy with Loeys-Dietz syndrome.
J Cardiothorac Surg. 2024 Sep 18;19(1):530. doi: 10.1186/s13019-024-03033-x.
9
Complex Multi-Stage Total Aortic and Subclavian Artery Replacement in a 9-year old boy with Loeys-Dietz-Syndrome.
Ann Vasc Surg. 2022 Mar;80:396.e1-396.e6. doi: 10.1016/j.avsg.2021.10.051. Epub 2021 Nov 20.
10
Valve-sparing aortic root replacement and aortic valve repair for a 2-year-old girl with Loeys-Dietz syndrome.
Interact Cardiovasc Thorac Surg. 2022 Jun 1;34(6):1174-1176. doi: 10.1093/icvts/ivab367.

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验