Cardiac Surgery Unit, Guangdong Provincial People's Hospital, No.106, Zhongshan 2nd Road, Guangzhou, Guangdong Province, China.
J Cardiothorac Surg. 2024 Sep 18;19(1):530. doi: 10.1186/s13019-024-03033-x.
Connective tissue disorders such as Marfan- and Loeys-Dietz syndrome (LDS) can lead to aortic aneurysms and aortic dissections in children. Patients with LDS often necessitating multiple aortic surgeries throughout their lives to extend their lifespan. A boy with LDS underwent Bentall procedure at the age of three for aortic aneurysm. At the age of six, this boy was referred to the hospital again due to severe abdominal pain. Computed tomographic angiography (CTA)indicates aortic dissection (DeBakey Type III, Stanford Type B). After a multidisciplinary team discussion, a successful thoracoabdominal aortic replacement was performed.
结缔组织疾病，如马凡综合征和洛伊茨-戴茨综合征（LDS），可导致儿童的主动脉瘤和主动脉夹层。LDS 患者往往需要多次主动脉手术来延长寿命。一名患有 LDS 的男孩在三岁时因主动脉瘤接受了 Bentall 手术。在六岁时，这名男孩因严重腹痛再次被送往医院。计算机断层血管造影（CTA）显示主动脉夹层（DeBakey Ⅲ型，斯坦福 B 型）。经过多学科团队讨论，成功进行了胸腹主动脉置换术。
