Department of Cardiovascular Surgery, Mt. Fuji Shizuoka Children's Hospital, Shizuoka City, Japan.
Department of Cardiovascular Surgery, Mt. Fuji Shizuoka Children's Hospital, Shizuoka City, Japan.
Ann Thorac Surg. 2019 Apr;107(4):e251-e253. doi: 10.1016/j.athoracsur.2018.08.093. Epub 2018 Oct 25.
An infant boy with 21 trisomy was diagnosed with complete atrioventricular septal defect-Rastelli type A with parachute left atrioventricular valve and absent left mural leaflet. Biventricular repair was difficult in infancy because the left ventricular volume and left atrioventricular valve annulus were too small. After 2 pulmonary artery bandings, the left atrioventricular valve annulus increased to 85% of normal mitral valve, and the left ventricular end-diastolic volume increased to 98% of normal. We report a successful instance of complete atrioventricular septal defect that achieved biventricular repair via novel left atrioventricular valvuloplasty for parachute left atrioventricular valve and absent left mural leaflet.
一名患有 21 三体综合征的男婴被诊断为完全性房室间隔缺损-Rastelli 型 A，伴有降落伞状左房室瓣和左房室瓣瓣叶缺如。由于左心室容量和左房室瓣环过小，婴儿期行双心室修复较为困难。两次肺动脉带缩术后，左房室瓣环增加至正常二尖瓣的 85%，左心室舒张末期容积增加至正常的 98%。我们报告了一例成功的完全性房室间隔缺损病例，通过新颖的左房室瓣瓣成形术治疗降落伞状左房室瓣和左房室瓣瓣叶缺如，实现了双心室修复。
