Hong Sung Jin, Lee Ji Young, Kim Dae Sung
Department of Anesthesiology and Pain Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea.
Korean J Anesthesiol. 2009 Sep;57(3):395-397. doi: 10.4097/kjae.2009.57.3.395.
Spinal muscular atrophy (SMA) is a rare lower motor neuron disease without sensory loss that needs special care of anesthesiologists due to increased sensitivity to muscle relaxants, potential for aspiration and respiratory weakness. We anesthetized a 10 year-old girl with type 3 SMA for resection of sebaceous cyst in her occiput. We used intravenous anesthetic technique and intubated the patient without any muscle relaxants. The anesthetic and recovery courses were successful. So we present our general anesthetic case under the endotracheal intubation without any muscle relaxants as one of the anesthetic methods for the patients with SMA.
脊髓性肌萎缩症（SMA）是一种罕见的下运动神经元疾病，无感觉丧失，由于对肌肉松弛剂敏感性增加、有误吸风险和呼吸肌无力，需要麻醉医生给予特别护理。我们为一名患有3型SMA的10岁女孩进行麻醉，以切除其枕部的皮脂腺囊肿。我们采用静脉麻醉技术，在未使用任何肌肉松弛剂的情况下为患者插管。麻醉和恢复过程顺利。因此，我们将在无任何肌肉松弛剂的情况下进行气管插管的全身麻醉病例作为SMA患者的麻醉方法之一进行介绍。
