Ozalp Hakan, Hamzaoglu Vural, Karatas Derya, Dagtekin Ahmet, Yildız Mehmet, Avcı Emel
Department of Neurosurgery, Mersin University School of Medicine, Mersin, Turkey.
Department of Pathology, Mersin University School of Medicine, Mersin, Turkey.
NMC Case Rep J. 2018 Dec 18;6(1):1-4. doi: 10.2176/nmccrj.cr.2018-0105. eCollection 2019 Jan.
Neuroenteric cysts (NCs) are benign, rare congenital lesions which are most commonly found in the lower cervical and upper thoracic segments. Even though these are benign lesions, it may present with fatal neurologic deterioration particularly in pediatric patients.
We here report a 16-year-old boy who has unique manifestation with acute tetraplegia and respiratory arrest in emergency room. According to English literature, this is the first case of cervicomedullary intradural neuroenteric cyst which causes acute tetraplegia and respiratory arrest in a child.
The NCs can be manifested with unpredictable, life threating clinical presentation. The exact pathophysiology of an acute neurological deterioration is still unclear, however prolonged latent period with minor symptom should be considered carefully in child population.
神经肠囊肿(NCs)是一种良性、罕见的先天性病变,最常见于下颈椎和上胸段。尽管这些是良性病变,但它可能会导致致命的神经功能恶化,尤其是在儿科患者中。
我们在此报告一名16岁男孩,他在急诊室出现了急性四肢瘫痪和呼吸骤停的独特表现。根据英文文献,这是首例导致儿童急性四肢瘫痪和呼吸骤停的颈髓硬膜内神经肠囊肿病例。
神经肠囊肿可表现出不可预测的、危及生命的临床表现。急性神经功能恶化的确切病理生理学仍不清楚,然而,在儿童群体中应仔细考虑症状轻微的较长潜伏期。