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A Case for Not Going Global: "Americanization" of Diet Accelerates Hepatic Mitochondrial Injury in a Model of Wilson Disease.不走向全球的一个例子：饮食“美国化”加速威尔逊病模型中的肝脏线粒体损伤。
Cell Mol Gastroenterol Hepatol. 2019;7(3):684-685. doi: 10.1016/j.jcmgh.2019.01.001. Epub 2019 Jan 29.
2
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Int J Biochem Cell Biol. 2018 Sep;102:71-75. doi: 10.1016/j.biocel.2018.07.001. Epub 2018 Jul 8.
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Microbial peptide de-coppers mitochondria: implications for Wilson disease.微生物肽使线粒体脱铜：对威尔逊病的影响
J Clin Invest. 2016 Jul 1;126(7):2412-4. doi: 10.1172/JCI88617. Epub 2016 Jun 20.
4
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Mitochondrial structure and function in the untreated Jackson toxic milk (tx-j) mouse, a model for Wilson disease.未处理的杰克逊毒奶（tx-j）小鼠（一种威尔逊病模型）的线粒体结构与功能
Mol Genet Metab. 2008 Jan;93(1):54-65. doi: 10.1016/j.ymgme.2007.08.127. Epub 2007 Nov 5.
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[Wilson-Konovalov cirrhosis].
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7
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Curr Gene Ther. 2007 Jun;7(3):217-20. doi: 10.2174/156652307780859053.
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[On hepatolenticular degeneration (Westphal-Struempell-Wilson diseas)].[关于肝豆状核变性（韦斯特法尔 - 施特伦佩尔 - 威尔逊病）]
Psychiatr Neurol Med Psychol (Leipz). 1959 Sep;11:273-7.
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[Heredity in hepatolenticular degeneration and the problem of the intrinsic relations between Westphal-Strumpell's pseudosclerosis and Wilson's disease; the nosologic location of Kehrer's "abdominal-Wilson" within hepatolenticular degeneration].[肝豆状核变性中的遗传以及韦斯法尔-施特吕姆佩尔假性硬化症与威尔逊病之间的内在关系问题；克勒尔“腹部威尔逊病”在肝豆状核变性中的疾病分类位置]
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Methanobactin reverses acute liver failure in a rat model of Wilson disease.甲醇菌素可逆转威尔逊病大鼠模型中的急性肝衰竭。
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本文引用的文献

1
A High-Calorie Diet Aggravates Mitochondrial Dysfunction and Triggers Severe Liver Damage in Wilson Disease Rats.高热量饮食加剧威尔逊病大鼠的线粒体功能障碍并引发严重肝损伤。
Cell Mol Gastroenterol Hepatol. 2019;7(3):571-596. doi: 10.1016/j.jcmgh.2018.12.005. Epub 2018 Dec 23.
2
Defining the human copper proteome and analysis of its expression variation in cancers.人类铜蛋白质组的定义及其在癌症中表达变化的分析。
Metallomics. 2017 Feb 22;9(2):112-123. doi: 10.1039/c6mt00202a.
3
Methanobactin reverses acute liver failure in a rat model of Wilson disease.甲醇菌素可逆转威尔逊病大鼠模型中的急性肝衰竭。
J Clin Invest. 2016 Jul 1;126(7):2721-35. doi: 10.1172/JCI85226. Epub 2016 Jun 20.
4
How Mammalian Cells Acquire Copper: An Essential but Potentially Toxic Metal.哺乳动物细胞如何获取铜：一种必需但可能有毒的金属。
Biophys J. 2016 Jan 5;110(1):7-13. doi: 10.1016/j.bpj.2015.11.025.
5
A four-helix bundle stores copper for methane oxidation.四螺旋束储存用于甲烷氧化的铜。
Nature. 2015 Sep 3;525(7567):140-3. doi: 10.1038/nature14854. Epub 2015 Aug 26.
6
Hepatic steatosis in Wilson disease--Role of copper and PNPLA3 mutations.Wilson 病中的肝脂肪变性——铜和 PNPLA3 突变的作用。
J Hepatol. 2015 Jul;63(1):156-63. doi: 10.1016/j.jhep.2015.01.034. Epub 2015 Feb 9.
7
Metabolic profiling reveals that PNPLA3 induces widespread effects on metabolism beyond triacylglycerol remodeling in Huh-7 hepatoma cells.代谢组学分析显示，PNPLA3 在 Huh-7 肝癌细胞中除了三酰基甘油重塑之外，还广泛影响代谢。
Am J Physiol Gastrointest Liver Physiol. 2014 Jul 1;307(1):G66-76. doi: 10.1152/ajpgi.00335.2013. Epub 2014 Apr 24.
8
Modifying factors and phenotypic diversity in Wilson's disease.Wilson 病的修饰因子和表型多样性。
Ann N Y Acad Sci. 2014 May;1315:56-63. doi: 10.1111/nyas.12420. Epub 2014 Apr 4.
9
Apolipoprotein E gene (APOE) genotype in Wilson's disease: impact on clinical presentation.载脂蛋白 E 基因 (APOE) 基因型在威尔逊病中的作用：对临床表现的影响。
Parkinsonism Relat Disord. 2012 May;18(4):367-9. doi: 10.1016/j.parkreldis.2011.12.005. Epub 2012 Jan 4.
10
Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease.Wilson 病大鼠模型中肝线粒体膜交联和破坏。
J Clin Invest. 2011 Apr;121(4):1508-18. doi: 10.1172/JCI45401.

A Case for Not Going Global: "Americanization" of Diet Accelerates Hepatic Mitochondrial Injury in a Model of Wilson Disease.

作者信息

To Uyen, Schilsky Michael L

机构信息

Departments of Medicine and Surgery, Divisions of Digestive Diseases and Transplant and Immunology, Yale University, New Haven, Connecticut.

Departments of Medicine and Surgery, Divisions of Digestive Diseases and Transplant and Immunology, Yale University, New Haven, Connecticut.

出版信息

Cell Mol Gastroenterol Hepatol. 2019;7(3):684-685. doi: 10.1016/j.jcmgh.2019.01.001. Epub 2019 Jan 29.

DOI:10.1016/j.jcmgh.2019.01.001
PMID:30707887
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6477543/
Abstract
摘要