Alkhotani Afnan, Butt Babar, Khalid Muhammad, Binmahfoodh Mohammed
Neuroscience Department, Neurosurgery Section, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia.
Neuroscience Department, Neurosurgery Section, King Faisal Specialist Hospital and Research Center, Jeddah, Saudi Arabia.
Int J Surg Case Rep. 2019;55:23-27. doi: 10.1016/j.ijscr.2019.01.003. Epub 2019 Jan 18.
Hydatid cyst represents the parasitic infection by Genus Echenococcus Granulosis. This disease usually involves liver followed by lungs and rarely the CNS. The CNS involvement by the Hydatid Cyst is present in 1-2% of all hydatidosis. Even when it is found in the Brain it presents usually in the supratentorial compartment. However this case was unique in having the Hydatid cyst within the infratentorial fossa. With multiple small cysts, causing mass effect and challenging for surgical resection.
A 44 years female presented with headache, diplobia and bulbar symptoms, followed by ataxia. Full examination, proper investigations showed the peripontomedullary hydatid cysts. Surgical management is illustrated.
It is still challenging for the neurosurgeons to operate on these lesions in spite of modern technologies and fancy approaches due to its delicate nature, associated risk of allergic reaction, cyst's material dissemination and irreversible injury of multiple neurological structure due to prolonged compression of cranial nerves crossing the cerebellopontine angle.
In this case report we are presenting a rare case of Multiple Hydatid cysts involving a rare location in the brain; peripontomedullary area and extending all the way down to the foramen magnum. Supported with a literature review in relation to disease etiology, epidemiology, clinical presentation and management.
包虫囊肿是由细粒棘球绦虫属引起的寄生虫感染。这种疾病通常累及肝脏,其次是肺,很少累及中枢神经系统。中枢神经系统包虫囊肿在所有包虫病病例中占1-2%。即使在脑部发现,通常也出现在幕上腔。然而,该病例的独特之处在于包虫囊肿位于幕下窝内。囊肿数量众多,产生占位效应,给手术切除带来挑战。
一名44岁女性出现头痛、复视和延髓症状,随后出现共济失调。全面检查和适当的检查显示桥延髓周围有包虫囊肿,并说明了手术治疗情况。
尽管有现代技术和先进方法,但由于这些病变性质脆弱、存在过敏反应风险、囊肿内容物播散以及由于穿过桥小脑角的颅神经长期受压导致多个神经结构不可逆转的损伤,神经外科医生对这些病变进行手术仍然具有挑战性。
在本病例报告中,我们展示了一例罕见的多发性包虫囊肿病例,累及脑部一个罕见部位——桥延髓周围区域,并一直延伸至枕骨大孔。同时还辅以关于该疾病病因、流行病学、临床表现和治疗的文献综述。