Jain Mantu, Das Sudhanshu S, Gantaguru Amrit, Panda Ritesh, Behera Sudarsan
Orthopedics, All India Institute of Medical Sciences, Bhubaneswar, IND.
Orthopedics, All India Institute of Medical Sciences, Bhubaneswar , IND.
Cureus. 2018 Nov 28;10(11):e3651. doi: 10.7759/cureus.3651.
Desmoids are rare soft-tissue tumors of the abdominal wall that may sporadically occur extra-abdominally. It manifests as clonal fibroblastic proliferation with an infiltrative tendency and capacity to recur without metastasizing. An adolescent male presented with a gradually increasing globular, non-tender, firm, non-pulsatile swelling (8 × 5 × 3 cm) in the left popliteal fossa that had been present for five months. Following thorough investigation with imaging and Tru-cut biopsy, finally, an excisional biopsy was done. Histopathological examination confirmed a desmoid tumor, and the patient received adjuvant radiotherapy. At the one-year postoperative follow-up, there was no recurrence; the patient had been explained the prognosis. This case highlights a rare site of an extra-abdominal desmoid but with classical clinical presentation, imaging, intraoperative, and histopathological findings. Awareness and knowledge of this entity are of paramount importance for clinical practitioners.
硬纤维瘤是一种罕见的腹壁软组织肿瘤，也可能偶尔发生于腹部外。它表现为克隆性成纤维细胞增殖，具有浸润性倾向且有复发能力但不发生转移。一名青少年男性患者，左腘窝处出现一个逐渐增大的球形、无压痛、质硬、无搏动性肿物（8×5×3厘米），已存在5个月。经过影像学和粗针穿刺活检的全面检查后，最终进行了切除活检。组织病理学检查确诊为硬纤维瘤，患者接受了辅助放疗。术后一年随访时未发现复发；已向患者解释了预后情况。该病例突出了腹部外硬纤维瘤的罕见部位，但具有典型的临床表现、影像学表现、术中表现及组织病理学表现。临床医生对该疾病的认识和了解至关重要。
