Gupta Ashish, Sharma Sneha D, Bansal Pankaj, Sikka Seema
1Department of Oral and Maxillofacial Surgery, Sudha Rustagi College of Dental Sciences & Research, Faridabad, Haryana India.
Present Address: Faridabad, India.
J Maxillofac Oral Surg. 2019 Mar;18(1):52-56. doi: 10.1007/s12663-018-1086-3. Epub 2018 Mar 1.
A hemangiopericytoma is a type of soft tissue sarcoma that originates in the pericytes in the walls of capillaries which was characterized in 1942. It is commonly seen in the age group of 5th-6th decades of adults and only 5-10% of cases occur in children with extreme rare occurrence in head and neck region (16%). A rare case of hemangiopericytoma in a 4-year-old female patient is presented here and its clinical, histopathological and immunohistochemically features are discussed. Though surgical resection remains the mainstay, excisional biopsy was primarily performed to reach the final diagnosis. Even in the follow-up phase of 1 year, no recurrence or no metastatic changes were observed.
血管外皮细胞瘤是一种软组织肉瘤，起源于毛细血管壁的周细胞，于1942年被描述。它常见于成年人50至60岁年龄组，仅5%至10%的病例发生在儿童中，在头颈部区域极为罕见（16%）。本文报告了一例4岁女性患者的罕见血管外皮细胞瘤病例，并讨论了其临床、组织病理学和免疫组化特征。尽管手术切除仍是主要治疗方法，但最初进行切除活检以明确最终诊断。即使在1年的随访期内，也未观察到复发或转移变化。
