Murli Lakshmi, Ranjit M S, Shah Prashant
Department of Pediatric Cardiology and Cardiothoracic Surgery, Kauvery Hospital, Chennai, Tamil Nadu, India.
Ann Pediatr Cardiol. 2019 Jan-Apr;12(1):64-65. doi: 10.4103/apc.APC_119_18.
Unroofed coronary sinus, an unusual form of interatrial communication, is a rare cardiac anomaly. It is not a true defect of the atrial septum. It is described as a partial (focal or fenestrated) or complete absence of the roof of the coronary sinus, resulting in a communication between the coronary sinus and left atrium. It is presumably the least common variety of defects associated with interatrial shunting. Such defects are often difficult to diagnose and may even be overlooked during surgery for complex congenital heart disease. In most cases, they are associated with a persistent left superior vena cava, pulmonary or tricuspid atresia, and hearts with isomeric right atrial appendages. We report a case of this unusual form of interatrial communication without any associated anomalies in a 7-year-old girl child who presented to us with exertional dyspnea.
无顶冠状静脉窦是一种不常见的心房内交通形式，是一种罕见的心脏异常。它并非真正的房间隔缺损。它被描述为冠状静脉窦顶部部分（局灶性或筛孔状）或完全缺失，导致冠状静脉窦与左心房之间存在交通。据推测，它是与心房分流相关的最不常见的缺损类型。此类缺损常难以诊断，甚至在复杂先天性心脏病手术过程中可能被忽视。在大多数情况下，它们与永存左上腔静脉、肺动脉闭锁或三尖瓣闭锁以及右心耳异构的心脏相关。我们报告一例7岁女童出现劳力性呼吸困难，患有这种不寻常的心房内交通形式但无任何相关异常的病例。
