Aljefri Nour Abdullah, Abothenain Fayha Farraj, Hussein Ahmed Mohamed, Saleh Waleed, Alkattan Khaled, Mohammed Shamayel Faheem, Alhajji Mohammed
Alfaisal Medical School, Alfaisal University, Riyadh, Saudi Arabia.
Section of Thoracic Surgery, King Faisal Specialist Hospital and Research Center, Riyadh, Saudi Arabia.
Ann Thorac Med. 2019 Jan-Mar;14(1):94-98. doi: 10.4103/atm.ATM_106_18.
Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, managed successfully by bilateral lung transplant performed on a 26 year old Saudi male.
特发性胸膜-肺实质纤维弹性组织增生症(PPFE)是一种罕见的、进行性的且最近才被认识的特发性间质性肺疾病亚型,除肺移植外尚无成功治疗的记录。我们报告一例来自中东的特发性胸膜-肺实质纤维弹性组织增生症病例,该病例通过对一名26岁沙特男性进行双侧肺移植而成功治愈。