Mutavdzic Perica, Dragas Marko, Kukic Biljana, Stevanovic Ksenija, Končar Igor, Ilić Nikola, Tomic Ivan, Sladojevic Milos, Davidovic Lazar
Clinic for Vascular and Endovascular Surgery, Clinical Center of Serbia, Belgrade, Serbia.
Clinic for Vascular and Endovascular Surgery, Clinical Center of Serbia, Belgrade, Serbia; School of Medicine, University of Belgrade, Serbia.
Ann Vasc Surg. 2020 Feb;63:454.e1-454.e4. doi: 10.1016/j.avsg.2018.11.019. Epub 2019 Feb 11.
We present a case of successfully treated abdominal aortic aneurysm in a 24-year-old patient with Marfan syndrome. After initial physical and ultrasound examination, the multislice computed tomography (MSCT) scan revealed infrarenal aortic aneurysm of 6 cm in diameter, 10 cm long, along with slightly dilated iliac arteries. However, dimensions of aortic root, aortic arch, and descending suprarenal aorta were within normal limits. Further on, because the patient presented with signs of impending rupture, an urgent surgical intervention was performed. The patient was discharged in good general medical condition 7 days after surgery. After 6 months of follow-up, the patient's condition was satisfying and no MSCT signs of further aortic dissection/aneurysm were identified. To the best of our knowledge, a case of successful management of a patient with Marfans syndrome and truly isolated infrarenal and symptomatic abdominal aortic aneurysm has not been described in the literature before.
我们报告一例成功治疗的24岁马凡综合征患者腹主动脉瘤病例。经过初步体格检查和超声检查后，多层螺旋计算机断层扫描（MSCT）显示肾下主动脉瘤，直径6厘米，长10厘米，同时髂动脉轻度扩张。然而，主动脉根部、主动脉弓和肾上腺上方降主动脉的尺寸在正常范围内。此外，由于患者出现即将破裂的迹象，因此进行了紧急手术干预。患者术后7天出院，一般身体状况良好。经过6个月的随访，患者情况令人满意，未发现MSCT显示进一步主动脉夹层/动脉瘤的迹象。据我们所知，此前文献中尚未描述过成功治疗马凡综合征患者且真正孤立的肾下和有症状腹主动脉瘤的病例。
