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四维度血流心脏磁共振评估机械性溶血性贫血。

Mechanical haemolytic anaemia assessed with four-dimensional flow cardiac magnetic resonance.

机构信息

Department of Cardiac Surgery, Nagoya University Graduate School of Medicine, Nagoya, Aichi, Japan.

Department of Fundamental Development for Advanced Low Invasive Diagnostic Imaging, Nagoya University Graduate School of Medicine, Nagoya, Aichi, Japan.

出版信息

Eur J Cardiothorac Surg. 2019 Oct 1;56(4):813-814. doi: 10.1093/ejcts/ezz031.

DOI:10.1093/ejcts/ezz031
PMID:30770716
Abstract

A 66-year-old woman developed marked haemolytic anaemia 2 years after total aortic arch replacement using a branched Dacron graft. Echocardiography confirmed bicuspid aortic valve stenosis. A four-dimensional flow magnetic resonance imaging revealed a jet flow arising from the aortic valve along with the vortex and turbulent flow inside the kinked prosthetic graft at the ascending aorta. She underwent a reoperation to replace the aortic valve and correct the kinking. The estimated energy loss after intervention was relieved to 2.9 mJ/cardiac cycle from 4.3 mJ/cardiac cycle before intervention. The patient's anaemia resolved immediately after the reoperation.

摘要

一位 66 岁女性在使用分支涤纶移植物进行全主动脉弓置换 2 年后出现明显溶血性贫血。超声心动图证实为二叶式主动脉瓣狭窄。四维血流磁共振成像显示,在升主动脉处扭曲的人造移植物内存在起源于主动脉瓣的射流以及涡流和湍流。她接受了再次手术以更换主动脉瓣并纠正扭曲。干预后估计的能量损失从干预前的 4.3mJ/心动周期缓解至 2.9mJ/心动周期。患者在再次手术后立即解决了贫血问题。

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引用本文的文献

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2
Hemolytic Anemia After an Aortic Dissection Treated With a Valve-Sparing Aortic Root Replacement.保留瓣膜的主动脉根部置换术治疗主动脉夹层后发生的溶血性贫血。
JACC Case Rep. 2023 Jun 12;18:101921. doi: 10.1016/j.jaccas.2023.101921. eCollection 2023 Jul 19.
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Utility of 4D Flow MRI in Thoracic Aortic Diseases: A Literature Review of Clinical Applications and Current Evidence.
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