Vasani Viral, Konar Subhas, Nandeesh Bevinahalli Nanjegowda, Praharaj Shanti Sankar
Department of Neurosurgery, Fortis Hospital, Bangalore, India,
Department of Neurosurgery, National Institute of Mental Health and Neurosciences (NIMHANS), Bangalore, India.
Pediatr Neurosurg. 2019;54(2):121-124. doi: 10.1159/000495791. Epub 2019 Feb 15.
A spinal neurenteric cyst is a rare entity. It commonly presents already at 5 weeks of age up to the 6th decade of life. The most common location is the cervical region followed by thoracic and lumbosacral regions. We report a 9-month-old male infant with sudden onset of weakness in both lower limbs. MRI revealed 2 cystic lesions at cervical and thoracic level with spinal cord compression. He underwent laminectomy and excision of the cervical lesion. The child improved significantly. The postoperative MRI shows complete excision of a dorsal lesion and presence of a cervical lesion. Later, he underwent cervical laminotomy and partial wall excision followed by shunt placement. The histopathological report revealed a neurenteric cyst. Two neurenteric cysts presented in the neuroaxis of the same patient: one was located ventral (thoracic) and the other dorsal (cervical). At the 2-year follow-up, the child was active and walking without support. Multiple cystic lesions in the neuroaxis can be neurenteric cysts.
脊髓神经管原肠囊肿是一种罕见的疾病。它通常在5周龄至60岁之间出现。最常见的部位是颈部，其次是胸部和腰骶部。我们报告一名9个月大的男婴，双下肢突然出现无力。MRI显示颈段和胸段有2个囊性病变并伴有脊髓受压。他接受了椎板切除术和颈段病变切除术。患儿明显好转。术后MRI显示背部病变完全切除，颈段病变仍存在。后来，他接受了颈椎板切开术和部分囊壁切除术，随后进行了分流管置入。组织病理学报告显示为神经管原肠囊肿。同一患者的神经轴出现了两个神经管原肠囊肿：一个位于腹侧（胸段），另一个位于背侧（颈段）。在2年的随访中，患儿活动自如，无需支撑即可行走。神经轴内的多个囊性病变可能是神经管原肠囊肿。
