Müller L C, Salzer G M
Department of Surgery II, Innsbruck University, Austria.
Eur J Cardiothorac Surg. 1988;2(4):284-6. doi: 10.1016/1010-7940(88)90085-1.
A case of a 22-year-old male with cicatricial pemphigoid and involvement of the bronchial system is reported. Manifestations of cicatricial pemphigoid in the mucous membranes of the airway distal to the larynx have not been hitherto described. The patient developed severe stenosis of the left mainstem bronchus 2 years after onset of the disease. Successful treatment by sleeve resection and end-to-end anastomosis was achieved. Diagnostic bronchoscopy in patients with severe dyspnoea suffering from cicatricial pemphigoid is recommended. Operative treatment of airway stenoses distal to the larynx caused by cicatritial pemphigoid is feasible.
报告了一例22岁男性瘢痕性类天疱疮累及支气管系统的病例。喉远端气道黏膜的瘢痕性类天疱疮表现此前未见报道。该患者在疾病发作2年后出现左主支气管严重狭窄。通过袖状切除术和端端吻合术成功实现了治疗。建议对患有瘢痕性类天疱疮且严重呼吸困难的患者进行诊断性支气管镜检查。瘢痕性类天疱疮所致喉远端气道狭窄的手术治疗是可行的。
