Dagmura Hasan, Daldal Emin, Akbaş Ahmet, Daşıran Fatih, Okan Ismail
General Surgery Department and Surgical Oncology, Gaziosmanpasa, University, Tokat, Turkey.
General Surgery Department, Gaziosmanpasa University, Tokat, Turkey.
J Surg Case Rep. 2019 Feb 12;2019(2):rjz014. doi: 10.1093/jscr/rjz014. eCollection 2019 Feb.
Agenesis of the gallbladder and cystic duct is a rare congenital anomaly occurring in <0.1% of the population. However, combined gallbladder and cystic duct agenesis (CDA) with polycystic liver disease associated with recurrent acute pancreatitis (RAP) has not been reported earlier. Herein we report a case of a 36-year-old female patient who was admitted to the hospital and successfully treated for acute pancreatitis most probably caused in the background of gallbladder and CDA with polycystic liver disease. In case of non-visualization of gallbladder with the presence of biliary symptoms after repeated ultrasonographic examinations, advanced techniques like MRCP, computed tomography, EUS and even endoscopic retrograde cholangiopancreatography (ERCP) to visualize biliary anatomy must be conducted before any surgical intervention. We present a case of gallbladder and CDA causing RAP by the formation of microlithiasis treated successfully with ERCP and without any unnecessary surgery, its management and review of the literature is assessed.
胆囊及胆囊管缺如是一种罕见的先天性异常，发生率低于人群的0.1%。然而，此前尚未有胆囊及胆囊管缺如合并多囊肝疾病伴复发性急性胰腺炎（RAP）的报道。在此，我们报告一例36岁女性患者，她因胆囊及胆囊管缺如合并多囊肝疾病，很可能在此背景下引发急性胰腺炎而入院，并成功接受治疗。在反复超声检查后出现胆道症状但胆囊未显影的情况下，在进行任何手术干预之前，必须采用如磁共振胰胆管造影（MRCP）、计算机断层扫描、内镜超声甚至内镜逆行胰胆管造影（ERCP）等先进技术来明确胆道解剖结构。我们呈现一例因微结石形成导致RAP的胆囊及胆囊管缺如病例，通过ERCP成功治疗，未进行任何不必要的手术，并对其管理及文献进行评估。
